Title : Pulmonary veno-occlusive disease in myeloproliferative disorder.
Language : English
Author, co-author : Willems, Evelyne [Centre Hospitalier Universitaire de Liège - CHU > > Hématologie clinique > > >]
Canivet, Jean-Luc [Centre Hospitalier Universitaire de Liège - CHU > > Soins intensifs >]
Ghaye, Benoît [Centre Hospitalier Universitaire de Liège - CHU > > Imagerie médicale >]
de Leval, Laurence [Centre Hospitalier Universitaire de Liège - CHU > > Anatomie pathologique >]
Radermecker, Marc [Centre Hospitalier Universitaire de Liège - CHU > > Chirurgie cardio-vasculaire >]
Preiser, Jean-Charles [Centre Hospitalier Universitaire de Liège - CHU > > Soins intensifs >]
Beguin, Yves [Centre Hospitalier Universitaire de Liège - CHU > > Hématologie clinique >]
Publication date : 2009
Journal title : European Respiratory Journal
Publisher : European Respiratory Society
Volume : 33
Issue/season : 1
Pages : 213-216
Peer reviewed : Yes (verified by ORBi)
Audience : International
ISSN : 0903-1936
e-ISSN : 1399-3003
City : Lausanne
Country : Switzerland
Abstract : [en] The present study reports a case of biopsy-proven pulmonary veno-occlusive disease as a cause of severe pulmonary hypertension in a patient suffering from a chronic myeloproliferative disorder. The pulmonary disease evolved favourably under treatment with defibrotide, a pro-fibrinolytic medication used in hepatic veno-occlusive disease.
Permalink : http://hdl.handle.net/2268/5983
DOI : 10.1183/09031936.00157707