Article (Scientific journals)
Acromegaly, multinodular goiter, and silent polyostotic fibrous dysplasia : a variant of the Mc Cune Albright syndrome.
Abs, R.; Beckers, Albert; Stevenaert, Achille et al.
1990In Journal of Endocrinological Investigation, 13 (8), p. 671-675
Peer Reviewed verified by ORBi
 

Files


Full Text
Acromegaly, multinodular goiter, and silent polyostotic fibrous dysplasia - a variant of the Mc Cune Albright syndrome..pdf
Publisher postprint (423.93 kB)
Download

All documents in ORBi are protected by a user license.

Send to



Details



Keywords :
Acromegaly; Human; Case study; Albright disease; Fibrous dysplasia; Clinical form; Goiter; Pituitary diseases; Thyroid diseases; Endocrinopathy; Diseases of the osteoarticular system
Abstract :
[en] A 36-year-old woman is reported with a possible variant of the McCune-Albright syndrome. The triad was incomplete because of the absence of skin pigmentation and since the sexual precocity was not evident. The presence of a pituitary mass and the secretory dynamics of growth hormone and prolactin were suggestive of a mammosomatotroph cell adenoma. A toxic multinodular goiter was also associated, but unique was the spontaneous normalization of the thyroid function. Unusual was the silent evolution of the polyostotic fibrous dysplasia, which was only fortuitously discovered during magnetic resonance imaging of the pituitary region. Treatment of the acromegaly with the long-acting somatostatin analogue octreotide resulted in an important inhibition of the GH secretion and in a reduction of the volume of the pituitary adenoma.
Disciplines :
Endocrinology, metabolism & nutrition
Author, co-author :
Abs, R.
Beckers, Albert ;  Université de Liège - ULiège > Département des sciences cliniques > Endocrinologie
Stevenaert, Achille ;  Université de Liège - ULiège > Neurochirurgie
Hennen, Georges ;  Université de Liège - ULiège > Endocrinologie clinique
Language :
English
Title :
Acromegaly, multinodular goiter, and silent polyostotic fibrous dysplasia : a variant of the Mc Cune Albright syndrome.
Publication date :
September 1990
Journal title :
Journal of Endocrinological Investigation
ISSN :
0391-4097
eISSN :
1720-8386
Publisher :
Kurtis, Milano, Italy
Volume :
13
Issue :
8
Pages :
671-675
Peer reviewed :
Peer Reviewed verified by ORBi
Available on ORBi :
since 27 May 2010

Statistics


Number of views
115 (0 by ULiège)
Number of downloads
420 (0 by ULiège)

Scopus citations®
 
26
Scopus citations®
without self-citations
24
OpenCitations
 
17

Bibliography


Similar publications



Contact ORBi