Pregnancy and delivery in a patient with a Fontan circulation and primary ciliary dyskinesia: A case report.

Congenital heart disease; Fontan; High risk pregnancy; Adult; Ciliary Motility Disorders/complications; Ciliary Motility Disorders/physiopathology; Female; Fontan Procedure/adverse effects; Fontan Procedure/methods; Humans; Pregnancy; Pregnancy Complications, Cardiovascular/physiopathology; Pregnancy Complications, Cardiovascular/surgery; Ciliary Motility Disorders; Fontan Procedure; Pregnancy Complications, Cardiovascular; Reproductive Medicine; Obstetrics and Gynecology

Abstract :

[en] A patient had primary ciliary dyskinesia with a complex cardiac malformation. As a child, she had benefited from a Fontan surgery to maintain a proper cardiac function. In such patients, whether it is safe to become pregnant is controversial. This case illustrates the possibility of carrying a pregnancy to term and providing a vaginal birth if a rigorous preconception consultation is performed to ensure care by a multidisciplinary specialized team, and the patient is properly informed of the risks.

Disciplines :

Reproductive medicine (gynecology, andrology, obstetrics)

Author, co-author :

Grandfils, Sébastien ; Centre Hospitalier Universitaire de Liège - CHU > > Service de gynécologie-obstétrique

Dewandre, Pierre-Yves ; Centre Hospitalier Universitaire de Liège - CHU > > Service d'anesthésie - réanimation

Bonnet, Pierre ; Université de Liège - ULiège > Département des sciences biomédicales et précliniques > Anatomie humaine générale

Radermecker, Marc ; Université de Liège - ULiège > Département des sciences biomédicales et précliniques > Anatomie humaine (thoracique et vasculaire de la tête et du cou)

Nisolle, Michelle ; Université de Liège - ULiège > Département des sciences cliniques > Gynécologie-obstétrique, partim Gynécologie

Kridelka, Frédéric ; Université de Liège - ULiège > Département des sciences cliniques > Gynécologie-Obstétrique

Emonts, Patrick ; Université de Liège - ULiège > Département des sciences cliniques > Gynécologie - Obstétrique, partim Obstétrique

Language :

English

Title :

Pregnancy and delivery in a patient with a Fontan circulation and primary ciliary dyskinesia: A case report.

Publication date :

November 2021

Journal title :

Journal of Gynecology Obstetrics and Human Reproduction

eISSN :

2468-7847

Publisher :

Elsevier Masson s.r.l., France

Volume :

Issue :

Pages :

102184

Peer reviewed :

Peer Reviewed verified by ORBi

Additional URL :

https://api.elsevier.com/content/article/PII:S2468784721001227?httpAccept=text/xml

Available on ORBi :

since 30 December 2024

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