La tachycardie ventriculaire catecholergique du jeune enfant: un diagnostic souvent meconnu

[en] Catecholaminergic polymorphic ventricular tachycardia is important to be diagnosed as an underlying disease in children with syncope and normal heart, because of its poor prognosis. CASE REPORT: A 3-year-old boy was referred for stress and emotion induced syncope. Primary ventricular arrhythmia, consisting of salvos of bidirectional ventricular tachycardia, was reproducibly induced by physical exertion. The syncopal events and severe arrhythmia disappeared with beta-blocking therapy. CONCLUSION: Despite its rare occurrence, catecholaminergic polymorphic ventricular tachycardia is an important cause of stress and emotion induced syncope and sudden death in children.

Disciplines :

Pediatrics
Cardiovascular & respiratory systems

Author, co-author :

Massin, M.

Leroy, P.

Misson, Jean-Paul ; Université de Liège - ULiège > Département des sciences cliniques > Pédiatrie

Lepage, P.

Language :

French

Title :

La tachycardie ventriculaire catecholergique du jeune enfant: un diagnostic souvent meconnu

Alternative titles :

[en] Catecholaminergic polymorphic ventricular tachycardia in a child: An often unrecognized diagnosis

Publication date :

June 2003

Journal title :

Archives de Pédiatrie

ISSN :

0929-693X

eISSN :

1769-664X

Publisher :

Elsevier Masson, France

Volume :

Issue :

Pages :

524-526

Peer reviewed :

Peer Reviewed verified by ORBi

Available on ORBi :

since 10 October 2010

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Bibliography

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