Keywords :
ACTH Syndrome, Ectopic/complications; Adenoma/complications/diagnosis/secretion/surgery; Adrenal Cortex Neoplasms/complications/surgery; Adrenocortical Hyperfunction/complications/drug therapy; Adrenocorticotropic Hormone/blood/secretion; Adult; Algorithms; Carcinoid Tumor/secretion; Child; Corticotropin-Releasing Hormone/diagnostic use; Cushing Syndrome/classification/diagnosis/drug therapy/etiology; Dexamethasone/diagnostic use; Diagnosis, Differential; Diagnostic Imaging; Dopamine Agonists/therapeutic use; Female; Humans; Hypothalamo-Hypophyseal System/drug effects/physiopathology; Magnetic Resonance Imaging; Male; Petrosal Sinus Sampling; Pituitary Neoplasms/complications/diagnosis/secretion/surgery; Pituitary-Adrenal Function Tests; Pituitary-Adrenal System/drug effects/physiopathology; Pregnancy; Pregnancy Complications, Neoplastic; Vasopressins/diagnostic use; Exploration radioisotopique; Radiodiagnostic; Imagerie médicale; Hypercorticisme; Corticosurrénale pathologie; Surrénale pathologie; Tumeur bénigne; Endocrinopathie; Hypophyse pathologie; Homme; Traitement; Diagnostic; Analyse biochimique; Positon; Emission; Tomoscintigraphie; Tomodensitométrie; Imagerie RMN; Cushing syndrome; Hypophyse; Adénome
Abstract :
[en] Cushing's disease remains a difficult diagnosis in spite of new technical procedures such as pituitary MRI, selective bilateral petrosal or cavernous sampling, (111)In pentreotide scan and 18 Flurodeoxyglucose pituitary PET scan. In this article, we review biological diagnostic procedures of Cushing's disease and corticotroph adenomas. According to our experience and the literature, we summarize the approach in medical treatment of Cushing's disease.
[fr] Le diagnostic de la maladie de Cushing reste difficile en dépit des nombreuses avancées techniques telles que l'IRM hypophysaire, le cathétérisme sélectif des sinus pétreux inférieurs ou encore des sinus caverneux, le 111In pentréotide scan et le PET scan avec 18 flurodéoxyglucose hypophysaires. Dans cet article, nous passons en revues les méthodes de diagnostic biologique de la maladie de Cushing et des adénomes corticotropes, les diagnostics différentiels ainsi que le traitement médical selon notre expérience et les données les plus récentes de la littérature.
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