Cystic kidney diseases in children.

ADPKD; ARPDK; Bardet–Biedl syndrome; Cystic dysplasia; HNF1-beta; Kidney cyst; Multicystic dysplastic kidney; Nephronophthisis; Simple kidney cyst; tuberous sclerosis complex; Child; Humans; Prognosis; Disease Progression; Kidney; Kidney Diseases, Cystic/diagnosis; Kidney Diseases, Cystic/therapy; Kidney Diseases, Cystic; Pediatrics, Perinatology and Child Health

Abstract :

[en] Cystic kidney disease comprises a broad group of heterogeneous diseases, which differ greatly in age at onset, disease manifestation, systemic involvement, disease progression, and long-term prognosis. As our understanding of these diseases continues to evolve and new treatment strategies continue to emerge, correctly differentiating and diagnosing these diseases becomes increasingly important. In this review, we aim to highlight the key features of the most relevant cystic kidney diseases, underscore important diagnostic characteristics of each disease, and present specific management options if applicable.

Disciplines :

Urology & nephrology
Pediatrics

Author, co-author :

De Groof, J; Department of Pediatric Nephrology, University Hospitals Leuven, Leuven, Belgium

Dachy, Angélique ; Centre Hospitalier Universitaire de Liège - CHU > > Service de pédiatrie

Breysem, L ; Department of Pediatric Radiology, University Hospitals Leuven, Leuven, Belgium

Mekahli, D ; Department of Pediatric Nephrology, University Hospitals Leuven, Leuven, Belgium, PKD Research Group, Department of Cellular and Molecular Medicine, KU Leuven, Leuven, Belgium. Electronic address: djalila.mekahli@uzleuven.be

Language :

English

Title :

Cystic kidney diseases in children.

Publication date :

May 2023

Journal title :

Archives de Pédiatrie

ISSN :

0929-693X

eISSN :

1769-664X

Publisher :

Elsevier Masson s.r.l., France

Volume :

Issue :

Pages :

240 - 246

Peer reviewed :

Peer Reviewed verified by ORBi

Additional URL :

https://api.elsevier.com/content/article/PII:S0929693X23000313?httpAccept=text/xml

Data Set :

https://doi.org/10.1016/j.arcped.2023.02.005

Available on ORBi :

since 02 October 2023

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