Imaging the adult with congenital heart disease: a multimodality imaging  approach-position paper from the EACVI.

[en] Advances in the diagnosis and management of congenital heart disease have led to a marked improvement in the survival of adult with congenital heart disease (ACHD) patients. However, ACHD patients are a heterogeneous population, with a large spectrum of anatomic substrates even within specific lesions. In addition, the nature of previous surgery and other intervention is highly variable rendering each patient unique and residual anatomic and haemodynamic abnormalities are very common. As the ACHD population continues to age, acquired heart disease will also require cardiac imaging assessment. It is increasingly recognized in ACHD community that the diagnostic utility of a multimodality cardiovascular approach is greater than the sum of individual tests. In ACHD patients, diagnostic information can be obtained using a variety of diagnostic tools. The aims of this document are to describe the role of each diagnostic modality in the care of ACHD patients and to provide guidelines for a multimodality approach. The goal should be to provide the most appropriate and cost-effective diagnostic pathway for each individual ACHD patient.

Disciplines :

Cardiovascular & respiratory systems

Author, co-author :

Di Salvo, Giovanni; Department of Adult Congenital Heart Disease, National Heart and Lung Institute,

Miller, Owen; Department of Congenital Heart Disease, Evelina London Children's Hospital, Guy's

Babu Narayan, Sonya; Department of Adult Congenital Heart Disease, National Heart and Lung Institute,

Li, Wei; Department of Adult Congenital Heart Disease, National Heart and Lung Institute,

Budts, Werner; Department Cardiovascular Sciences (KU Leuven), Congenital and Structural

Valsangiacomo Buechel, Emanuela R; Pediatric Heart Center, University Children's Hospital Zurich, Steinwiesstrasse

Frigiola, Alessandra; Adult Congenital Heart Disease, Guy's and St Thomas' Hospital, Westminster Bridge

van den Bosch, Annemien E; Department of Cardiology, Erasmus Medical Center, Postbus 2040, CA Rotterdam, The

Bonello, Beatrice; Department of Paediatric Cardiology, Great Ormond Street Hospital, London, UK.

Mertens, Luc; Division of Cardiology, Labatt Family Heart Centre, Hospital for Sick Children

More authors (8 more)

Other collaborator :

Delgado, Victoria

Haugaa, Kristina H

LANCELLOTTI, Patrizio ; Centre Hospitalier Universitaire de Liège - CHU > > Service de cardiologie

Flachskampf, Frank

Cardim, Nuno

Gerber, Bernhard

Masci, Pier Giorgio

Donal, Erwan

Gimelli, Alessia

Muraru, Denisa

Cosyns, Bernard

Language :

English

Title :

Imaging the adult with congenital heart disease: a multimodality imaging approach-position paper from the EACVI.

Publication date :

01 October 2018

Journal title :

European heart journal. Cardiovascular Imaging

eISSN :

2047-2412

Volume :

Issue :

Pages :

1077-1098

Peer reviewed :

Peer reviewed

Funding number :

FS/11/38/28864/BHF_/British Heart Foundation/United Kingdom

Available on ORBi :

since 18 May 2022

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