Summary: International Consensus Statement on Nomenclature and Classification of  the Congenital Bicuspid Aortic Valve and Its Aortopathy, for Clinical, Surgical, Interventional and Research Purposes.

Michelena, Hector I; Della Corte, Alessandro; Evangelista, Arturo; Maleszewski, Joseph J; Edwards, William D; Roman, Mary J; Devereux, Richard B; Fernández, Borja; Asch, Federico M; Barker, Alex J; Sierra-Galan, Lilia M; De Kerchove, Laurent; Fernandes, Susan M; Fedak, Paul W M; Girdauskas, Evaldas; Delgado, Victoria; Abbara, Suhny; Lansac, Emmanuel; Prakash, Siddharth K; Bissell, Malenka M; Popescu, Bogdan A; Hope, Michael D; Sitges, Marta; Thourani, Vinod H; Pibarot, Phillippe; Chandrasekaran, Krishnaswamy; LANCELLOTTI, Patrizio; Borger, Michael A; Forrest, John K; Webb, John; Milewicz, Dianna M; Makkar, Raj; Leon, Martin B; Sanders, Stephen P; Markl, Michael; Ferrari, Victor A; Roberts, William C; Song, Jae-Kwan; Blanke, Philipp; White, Charles S; Siu, Samuel; Svensson, Lars G; Braverman, Alan C; Bavaria, Joseph; Sundt, Thoralf M; El Khoury, Gebrine; De Paulis, Ruggero; Enriquez-Sarano, Maurice; Bax, Jeroen J; Otto, Catherine M; Schäfers, Hans-Joachim

doi:10.1016/j.athoracsur.2021.05.001

Article (Scientific journals)

Summary: International Consensus Statement on Nomenclature and Classification of the Congenital Bicuspid Aortic Valve and Its Aortopathy, for Clinical, Surgical, Interventional and Research Purposes.

Michelena, Hector I; Della Corte, Alessandro; Evangelista, Arturo et al.

2021 • In Annals of Thoracic Surgery, 112 (3), p. 1005-1022

Peer Reviewed verified by ORBi

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https://hdl.handle.net/2268/290914

DOI
10.1016/j.athoracsur.2021.05.001

PubMed
34304861

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Keywords :

Bicuspid Aortic Valve Disease/classification/surgery; Biomedical Research; Humans; Systematized Nomenclature of Medicine

Abstract :

[en] This International evidence-based nomenclature and classification consensus on the congenital bicuspid aortic valve and its aortopathy recognizes 3 types of bicuspid aortic valve: 1. Fused type, with 3 phenotypes: right-left cusp fusion, right-non cusp fusion and left-non cusp fusion; 2. 2-sinus type with 2 phenotypes: Latero-lateral and antero-posterior; and 3. Partial-fusion or forme fruste. This consensus recognizes 3 bicuspid-aortopathy types: 1. Ascending phenotype; root phenotype; and 3. extended phenotypes.

Disciplines :

Cardiovascular & respiratory systems

Author, co-author :

Michelena, Hector I; Department of Cardiovascular Medicine, Mayo Clinic, Rochester, Minnesota.

Della Corte, Alessandro; Department of Translational Medical Sciences, University of Campania "L.

Evangelista, Arturo; Department of Cardiology, Hospital Vall d'Hebron, Vall d'Hebron Research

Maleszewski, Joseph J; Department of Laboratory Medicine and Pathology, Mayo Clinic, Rochester,

Edwards, William D; Department of Laboratory Medicine and Pathology, Mayo Clinic, Rochester,

Roman, Mary J; Division of Cardiology, Weill Cornell Medicine, New York, New York.

Devereux, Richard B; Division of Cardiology, Weill Cornell Medicine, New York, New York.

Fernández, Borja; Departamento de Biología Animal, Facultad de Ciencias, Instituto de Investigación

Asch, Federico M; MedStar Health Research Institute, Washington, DC.

Barker, Alex J; Department of Radiology, Children's Hospital Colorado, University of Colorado,

More authors (41 more)

Language :

English

Title :

Summary: International Consensus Statement on Nomenclature and Classification of the Congenital Bicuspid Aortic Valve and Its Aortopathy, for Clinical, Surgical, Interventional and Research Purposes.

Publication date :

September 2021

Journal title :

Annals of Thoracic Surgery

ISSN :

0003-4975

eISSN :

1552-6259

Publisher :

Elsevier, Nl

Volume :

112

Issue :

Pages :

1005-1022

Peer reviewed :

Peer Reviewed verified by ORBi

Commentary :

Copyright © 2021 The Society of Thoracic Surgeons, the American Association for Thoracic Surgery, the European Association for Cardio-Thoracic Surgery, and the Radiological Society of North America. Published by Elsevier Inc. Published by Elsevier Inc. All rights reserved.

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