International consensus statement on nomenclature and classification of the  congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes.

Michelena, Hector I; Della Corte, Alessandro; Evangelista, Arturo; Maleszewski, Joseph J; Edwards, William D; Roman, Mary J; Devereux, Richard B; Fernández, Borja; Asch, Federico M; Barker, Alex J; Sierra-Galan, Lilia M; De Kerchove, Laurent; Fernandes, Susan M; Fedak, Paul W M; Girdauskas, Evaldas; Delgado, Victoria; Abbara, Suhny; Lansac, Emmanuel; Prakash, Siddharth K; Bissell, Malenka M; Popescu, Bogdan A; Hope, Michael D; Sitges, Marta; Thourani, Vinod H; Pibarot, Phillippe; Chandrasekaran, Krishnaswamy; LANCELLOTTI, Patrizio; Borger, Michael A; Forrest, John K; Webb, John; Milewicz, Dianna M; Makkar, Raj; Leon, Martin B; Sanders, Stephen P; Markl, Michael; Ferrari, Victor A; Roberts, William C; Song, Jae-Kwan; Blanke, Philipp; White, Charles S; Siu, Samuel; Svensson, Lars G; Braverman, Alan C; Bavaria, Joseph; Sundt, Thoralf M; El Khoury, Gebrine; De Paulis, Ruggero; Enriquez-Sarano, Maurice; Bax, Jeroen J; Otto, Catherine M; Schäfers, Hans-Joachim

doi:10.1016/j.jtcvs.2021.06.019

Article (Scientific journals)

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes.

Michelena, Hector I; Della Corte, Alessandro; Evangelista, Arturo et al.

2021 • In Journal of Thoracic and Cardiovascular Surgery, 162 (3), p. 383-e414

Peer Reviewed verified by ORBi

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https://hdl.handle.net/2268/290871

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10.1016/j.jtcvs.2021.06.019

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34304896

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Keywords :

Aorta/diagnostic imaging/surgery; Aortic Diseases/classification/diagnostic imaging/surgery; Aortic Valve/abnormalities/diagnostic imaging/surgery; Aortography; Bicuspid Aortic Valve Disease/classification/diagnostic imaging/surgery; Cardiac Imaging Techniques; Consensus; Humans; Phenotype; Predictive Value of Tests; Prognosis; Terminology as Topic; aortopathy; bicuspid aortic valve; classification; nomenclature

Abstract :

[en] This International Consensus Classification and Nomenclature for the congenital bicuspid aortic valve condition recognizes 3 types of bicuspid valves: 1. The fused type (right-left cusp fusion, right-non-coronary cusp fusion and left-non-coronary cusp fusion phenotypes); 2. The 2-sinus type (latero-lateral and antero-posterior phenotypes); and 3. The partial-fusion (forme fruste) type. The presence of raphe and the symmetry of the fused type phenotypes are critical aspects to describe. The International Consensus also recognizes 3 types of bicuspid valve-associated aortopathy: 1. The ascending phenotype; 2. The root phenotype; and 3. Extended phenotypes.

Disciplines :

Cardiovascular & respiratory systems

Author, co-author :

Michelena, Hector I; Department of Cardiovascular Medicine, Mayo Clinic, Rochester, Minn. Electronic

Della Corte, Alessandro; Department of Translational Medical Sciences, University of Campania "L.

Evangelista, Arturo; Department of Cardiology, Hospital Vall d'Hebron, Vall d'Hebron Research

Maleszewski, Joseph J; Department of Laboratory Medicine and Pathology, Mayo Clinic, Rochester, Minn.

Edwards, William D; Department of Laboratory Medicine and Pathology, Mayo Clinic, Rochester, Minn.

Roman, Mary J; Division of Cardiology, Weill Cornell Medicine, New York, NY.

Devereux, Richard B; Division of Cardiology, Weill Cornell Medicine, New York, NY.

Fernández, Borja; Departamento de Biologia Animal, Facultad de Ciencias, Instituto de Investigación

Asch, Federico M; MedStar Health Research Institute, Washington, DC.

Barker, Alex J; Department of Radiology, Children's Hospital Colorado, University of Colorado,

More authors (41 more)

Language :

English

Title :

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes.

Publication date :

September 2021

Journal title :

Journal of Thoracic and Cardiovascular Surgery

ISSN :

0022-5223

eISSN :

1097-685X

Publisher :

Mosby, Us mo

Volume :

162

Issue :

Pages :

e383-e414

Peer reviewed :

Peer Reviewed verified by ORBi

Funding number :

R01 HL137028/HL/NHLBI NIH HHS/United States

Commentary :

Available on ORBi :

since 18 May 2022

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