Article (Scientific journals)
Myasthénie auto-immune juvénile.
Materne, Charlène; Hudon, L.; DARON, Aurore et al.
2020In Revue Médicale de Liège, 75 (7-8), p. 524-528
Peer reviewed
 

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Keywords :
Adrenal Cortex Hormones; Child; Diplopia; Female; Humans; Myasthenia Gravis; Thoracoscopy; Thymectomy; Diagnosis; Treatment; Juvenile myasthenia
Abstract :
[en] We report the story of an 11-year-old girl admitted to the emergency room for diplopia and divergent squint. Promptly apparead a fluctuating ptosis, a nasal voice and swallowing disorders, evoking the diagnosis of autoimmune myasthenia. The latter has been confirmed with electromyogram. Treatment with corticoids, plasmapheresis and pyridostigmine allowed symptoms control. Thymectomy by left thoracoscopy, non-robot assisted, was performed 6 months after the appearance of the first clinical signs for the purpose of remission.
Disciplines :
Neurology
Pediatrics
Author, co-author :
Materne, Charlène ;  Université de Liège - ULiège > Master spéc. pédia.
Hudon, L.
DARON, Aurore ;  Centre Hospitalier Universitaire de Liège - CHU > Département de Pédiatrie > Service de pédiatrie
Demarche, Martine ;  Université de Liège - ULiège > Département des sciences cliniques > Département des sciences cliniques
Language :
French
Title :
Myasthénie auto-immune juvénile.
Alternative titles :
[en] Juvenil autoimmune myasthenia
Publication date :
July 2020
Journal title :
Revue Médicale de Liège
ISSN :
0370-629X
eISSN :
2566-1566
Publisher :
Université de Liège. Revue Médicale de Liège, Liège, Belgium
Volume :
75
Issue :
7-8
Pages :
524-528
Peer reviewed :
Peer reviewed
Available on ORBi :
since 25 January 2021

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