[en] Cardiovascular disease is the main cause of morbidity and mortality in patients with Marfan syndrome. The most life threatening complication is aortic root aneurysms leading to aortic dissection or rupture. It can be prevented by regular aortic follow-up and prophylactic aortic surgery. Modern aortic surgery has led to a substantial increase in the life expectancy of these patients. We report two cases of Marfan syndrome with cardiovascular complications. Their management is discussed according to the most recent literature.
Disciplines :
Surgery
Author, co-author :
BRULS, Samuel ; Centre Hospitalier Universitaire de Liège - CHU > Chirurgie cardio-vasculaire
Radermecker, Marc ; Université de Liège - ULiège > Département des sciences biomédicales et précliniques > Anatomie humaine
Creemers, E.
Bonnet, Pierre ; Université de Liège - ULiège > Département des sciences biomédicales et précliniques > Anatomie humaine systématique
NELLESSEN, Eric ; Centre Hospitalier Universitaire de Liège - CHU > Cardiologie
VAN DAMME, Hendrik ; Centre Hospitalier Universitaire de Liège - CHU > Chirurgie cardio-vasculaire
de Leval, Laurence ; Université de Liège - ULiège > Département des sciences biomédicales et précliniques > Département des sciences biomédicales et précliniques
Defraigne, Jean-Olivier ; Université de Liège - ULiège > Département des sciences cliniques > Chirurgie cardio-vasculaire et thoracique
Language :
English
Title :
Surgical treatment of cardiovascular complications in patients with Marfan syndrome: a report of two cases and literature review.
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