Surgical treatment of cardiovascular complications in patients with Marfan syndrome: a report of two cases and literature review.

BRULS, Samuel; Radermecker, Marc; Creemers, E.; Bonnet, Pierre; NELLESSEN, Eric; VAN DAMME, Hendrik; de Leval, Laurence; Defraigne, Jean-Olivier

doi:10.1080/00015458.2012.11680826

Article (Scientific journals)

Surgical treatment of cardiovascular complications in patients with Marfan syndrome: a report of two cases and literature review.

BRULS, Samuel; Radermecker, Marc; Creemers, E. et al.

2012 • In Acta Chirurgica Belgica, 112 (3), p. 213-8

Peer Reviewed verified by ORBi

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https://hdl.handle.net/2268/140402

DOI
10.1080/00015458.2012.11680826

PubMed
22808762

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Keywords :

Blood Vessel Prosthesis Implantation; Heart Transplantation; Humans; Male; Marfan Syndrome/complications/diagnosis/surgery; Middle Aged; Young Adult

Abstract :

[en] Cardiovascular disease is the main cause of morbidity and mortality in patients with Marfan syndrome. The most life threatening complication is aortic root aneurysms leading to aortic dissection or rupture. It can be prevented by regular aortic follow-up and prophylactic aortic surgery. Modern aortic surgery has led to a substantial increase in the life expectancy of these patients. We report two cases of Marfan syndrome with cardiovascular complications. Their management is discussed according to the most recent literature.

Disciplines :

Surgery

Author, co-author :

BRULS, Samuel ; Centre Hospitalier Universitaire de Liège - CHU > Chirurgie cardio-vasculaire

Radermecker, Marc ; Université de Liège - ULiège > Département des sciences biomédicales et précliniques > Anatomie humaine

Creemers, E.

Bonnet, Pierre ; Université de Liège - ULiège > Département des sciences biomédicales et précliniques > Anatomie humaine systématique

NELLESSEN, Eric ; Centre Hospitalier Universitaire de Liège - CHU > Cardiologie

VAN DAMME, Hendrik ; Centre Hospitalier Universitaire de Liège - CHU > Chirurgie cardio-vasculaire

de Leval, Laurence ; Université de Liège - ULiège > Département des sciences biomédicales et précliniques > Département des sciences biomédicales et précliniques

Defraigne, Jean-Olivier ; Université de Liège - ULiège > Département des sciences cliniques > Chirurgie cardio-vasculaire et thoracique

Language :

English

Title :

Surgical treatment of cardiovascular complications in patients with Marfan syndrome: a report of two cases and literature review.

Publication date :

2012

Journal title :

Acta Chirurgica Belgica

ISSN :

1784-3421

eISSN :

2577-0160

Publisher :

Taylor & Francis, United Kingdom

Volume :

112

Issue :

Pages :

213-8

Peer reviewed :

Peer Reviewed verified by ORBi

Available on ORBi :

since 24 January 2013

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Bibliography

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