[en] Two cases of Lhermitte-Duclos disease confirmed by biopsy are reported. Review of the 58 published cases shows that the disease can manifest itself only by signs of increased intracranial pressure. Cerebellar symptoms are not constant. Computed tomographic (CT) scans suggest the diagnosis by showing a posterior fossa lesion, iso- and hypodense, partially calcified, and not enhanced by contrast medium. Magnetic resonance imaging (MRI) seems to define limits of the lesion better than CT scanning and could improve the surgical approach. Surgical excision of the lesion is the only satisfactory treatment. The postoperative prognosis is usually favorable.
Disciplines :
Neurology Surgery
Author, co-author :
Milbouw, G.
Born, J. D.
Martin, Didier ; Université de Liège - ULiège > Département des sciences cliniques > Neurochirurgie
Collignon, Jacques ; Centre Hospitalier Universitaire de Liège - CHU > Imagerie médicale
Hans, Pol ; Université de Liège - ULiège > Département des sciences cliniques > Anesthésie et réanimation
Reznik, Michel ; Université de Liège - ULiège > Services généraux (Faculté de médecine) > Relations académiques et scientifiques (Médecine)
Bonnal, Joël ; Université de Liège - ULiège > Relations académiques et scientifiques (Médecine)
Language :
English
Title :
Clinical and Radiological Aspects of Dysplastic Gangliocytoma (Lhermitte-Duclos Disease): A Report of Two Cases with Review of the Literature
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