[en] [en] BACKGROUND: Aggressive angiomyxoma is a rare, locally aggressive soft tissue tumour that chiefly involves the vulvoperineal region of young female patients. Treatment is wide surgical excision. Frequent relapses are common.
CASES: We present three patients who each had an aggressive angiomyxoma treated initially for another presumed diagnosis. Two patients required immediate repeat surgical procedures for incomplete tumour excision. The third patient developed a recurrence two years after the initial surgery. In one patient, hormonal therapy was used postoperatively because the evaluation of the tumour margins was uncertain. Harpoon markers were used to aid in tumour localization in another patient prior to resection.
CONCLUSION: Clinicians should consider the diagnosis of aggressive angiomyxoma when a patient presents with an atypical vulvoperineal mass, as an incorrect diagnosis may lead to repeated surgical procedures.
Disciplines :
Surgery
Author, co-author :
Alobaid, Abdulaziz; Department of Gynecology Oncology, Notre-Dame Hospital, CHUM, University of Montreal, Montreal, QC
Goffin, Frédéric ; Centre Hospitalier Universitaire de Liège - CHU > > Service de gynécologie-obstétrique (CHR) ; Department of Gynecology Oncology, Notre-Dame Hospital, CHUM, University of Montreal, Montreal, Canada
Lussier, Christian; Department of Gynecology Oncology, Notre-Dame Hospital, CHUM, University of Montreal, Montreal, Canada
Drouin, Pierre; Department of Gynecology Oncology, Notre-Dame Hospital, CHUM, University of Montreal, Montreal, Canada
Language :
English
Title :
Aggressive angiomyxoma of the vulva or perineum: report of three patients.
The women whose stories are told in this case report have provided signed permission for its publication. Frederic Goffin is supported by the FNRS (Fonds national de la recherche scientifique, Brussels, Belgium), the CHU of Liege (Mandat de Recherche Clinique), and by the Fondation Leon Fredericq.
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