[en] Cystic kidney disease comprises a broad group of heterogeneous diseases, which differ greatly in age at onset, disease manifestation, systemic involvement, disease progression, and long-term prognosis. As our understanding of these diseases continues to evolve and new treatment strategies continue to emerge, correctly differentiating and diagnosing these diseases becomes increasingly important. In this review, we aim to highlight the key features of the most relevant cystic kidney diseases, underscore important diagnostic characteristics of each disease, and present specific management options if applicable.
Disciplines :
Urologie & néphrologie Pédiatrie
Auteur, co-auteur :
De Groof, J; Department of Pediatric Nephrology, University Hospitals Leuven, Leuven, Belgium
Dachy, Angélique ; Centre Hospitalier Universitaire de Liège - CHU > > Service de pédiatrie
Breysem, L ; Department of Pediatric Radiology, University Hospitals Leuven, Leuven, Belgium
Mekahli, D ; Department of Pediatric Nephrology, University Hospitals Leuven, Leuven, Belgium, PKD Research Group, Department of Cellular and Molecular Medicine, KU Leuven, Leuven, Belgium. Electronic address: djalila.mekahli@uzleuven.be
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