International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes.
Michelena, Hector I; Della Corte, Alessandro; Evangelista, Arturoet al.
2021 • In European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery, 60 (3), p. 448-476
[en] This International Consensus Classification and Nomenclature for the congenital bicuspid aortic valve condition recognizes 3 types of bicuspid valves: 1. The fused type (right-left cusp fusion, right-non-coronary cusp fusion and left-non-coronary cusp fusion phenotypes); 2. The 2-sinus type (latero-lateral and antero-posterior phenotypes); and 3. The partial-fusion (forme fruste) type. The presence of raphe and the symmetry of the fused type phenotypes are critical aspects to describe. The International Consensus also recognizes 3 types of bicuspid valve-associated aortopathy: 1. The ascending phenotype; 2. The root phenotype; and 3. Extended phenotypes.
Disciplines :
Cardiovascular & respiratory systems
Author, co-author :
Michelena, Hector I ; Department of Cardiovascular Medicine, Mayo Clinic, Rochester, MN, USA.
Della Corte, Alessandro ; Department of Translational Medical Sciences, University of Campania "L.
Evangelista, Arturo; Department of Cardiology, Hospital Vall d'Hebron, Vall d'Hebron Research
Maleszewski, Joseph J ; Department of Laboratory Medicine and Pathology, Mayo Clinic, Rochester, MN, USA.
Edwards, William D; Department of Laboratory Medicine and Pathology, Mayo Clinic, Rochester, MN, USA.
Roman, Mary J; Division of Cardiology, Weill Cornell Medicine, New York, NY, USA.
Devereux, Richard B; Division of Cardiology, Weill Cornell Medicine, New York, NY, USA.
Fernández, Borja; Departamento de Biología Animal, Facultad de Ciencias, Instituto de Investigación
Asch, Federico M; MedStar Health Research Institute, Washington, DC, USA.
Barker, Alex J ; Department of Radiology, Children's Hospital Colorado, University of Colorado
Sierra-Galan, Lilia M ; Cardiovascular Division, American British Cowdray Medical Center, Mexico City
De Kerchove, Laurent ; Division of Cardiothoracic and Vascular Surgery, Cliniques Universitaires
Fernandes, Susan M; Division of Pediatric Cardiology, Department of Pediatrics, Stanford University, ; Division of Cardiovascular Medicine, Department of Medicine, Stanford University,
Fedak, Paul W M ; Department of Cardiac Sciences, Libin Cardiovascular Institute, Cumming School of
Girdauskas, Evaldas; Department of Cardiovascular Surgery, University Heart and Vascular Center
Delgado, Victoria ; Department of Cardiology, Leiden University Medical Center, Leiden, Netherlands.
Abbara, Suhny ; Cardiothoracic Imaging Division, Department of Radiology, UT Southwestern Medical
Lansac, Emmanuel ; Department of Cardiac Surgery, Institute Mutualiste Montsouris, Paris, France.
Prakash, Siddharth K ; Department of Internal Medicine, McGovern Medical School, The University of Texas
Bissell, Malenka M ; Department of Biomedical Imaging Science, Leeds Institute to Cardiovascular and
Popescu, Bogdan A ; Department of Cardiology, University of Medicine and Pharmacy "Carol
Hope, Michael D; Department of Radiology and Biomedical Imaging, University of California San
Sitges, Marta ; Cardiovascular Institute, Hospital Clínic, Universitat de Barcelona, IDIBAPS
Thourani, Vinod H; Department of Cardiovascular Surgery, Marcus Valve Center, Piedmont Heart
Pibarot, Phillippe ; Department of Cardiology, Québec Heart & Lung Institute, Laval University Québec
Chandrasekaran, Krishnaswamy; Department of Cardiovascular Medicine, Mayo Clinic, Rochester, MN, USA.
LANCELLOTTI, Patrizio ; Centre Hospitalier Universitaire de Liège - CHU > > Service de cardiologie ; Gruppo Villa Maria Care and Research, Maria Cecilia Hospital, Cotignola
Borger, Michael A; University Clinic of Cardiac Surgery, Leipzig Heart Center, Leipzig, Germany.
Forrest, John K; Yale University School of Medicine & Yale New Haven Hospital, New Haven, CT, USA.
Webb, John; St Paul's Hospital, University of British Columbia, Vancouver, Canada.
Milewicz, Dianna M; Department of Internal Medicine, McGovern Medical School, The University of Texas
Makkar, Raj ; Cedars Sinai Heart Institute, Los Angeles, CA, USA.
Leon, Martin B; Division of Cardiology, Columbia University Irving Medical Center/NY Presbyterian
Sanders, Stephen P; Cardiac Registry, Departments of Cardiology, Pathology and Cardiac Surgery, ; Department of Pediatrics, Harvard Medical School, Boston, MA, USA.
Markl, Michael; Department of Radiology, Feinberg School of Medicine, Northwestern University,
Ferrari, Victor A; Cardiovascular Medicine Division, University of Pennsylvania Medical Center and
Roberts, William C; Baylor Heart and Vascular Institute, Baylor University Medical Center, Texas A &
Song, Jae-Kwan; University of Ulsan College of Medicine, Asan Medical Center, Seoul, South Korea.
Blanke, Philipp; Department of Radiology, St. Paul's Hospital, Vancouver, BC, Canada.
White, Charles S; Department of Radiology, University of Maryland School of Medicine, Baltimore,
Siu, Samuel ; Schulich School of Medicine and Dentistry, London, ON, Canada.
Svensson, Lars G; Heart, Vascular and Thoracic Institute, Cleveland Clinic, Cleveland, OH, USA.
Braverman, Alan C ; Cardiovascular Division, Department of Medicine, Washington University School of
Bavaria, Joseph; Division of Cardiac Surgery, University of Pennsylvania, Philadelphia, PA, USA.
Sundt, Thoralf M; Division of Cardiac Surgery, Massachusetts General Hospital, Boston, MA, USA.
El Khoury, Gebrine; Division of Cardiothoracic and Vascular Surgery, Cliniques Universitaires
De Paulis, Ruggero ; Department of Cardiac Surgery, European Hospital and Unicamillus University Rome
Enriquez-Sarano, Maurice ; Department of Cardiovascular Medicine, Mayo Clinic, Rochester, MN, USA.
Bax, Jeroen J ; Department of Cardiology, Leiden University Medical Center, Leiden, Netherlands.
Otto, Catherine M; Division of Cardiology, University of Washington, Seattle, WA, USA.
Schäfers, Hans-Joachim ; Department of Thoracic and Cardiovascular Surgery, Saarland University Medical
Endorsed by the Heart Valve Society (HVS), European Association of Cardiovascular
International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes.
Publication date :
11 September 2021
Journal title :
European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery
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