Comprehensive multi-modality imaging approach in arrhythmogenic cardiomyoapthy : an expert consensus document of the European Association of Cardiovascular Imaging
Haugaa, KH; Basso, C; Badano, LPet al.
2017 • In European Heart Journal. Cardiovascular Imaging
[en] Arrhythmogenic cardiomyopathy (AC) is a progressive disease with high risk of life-threatening ventricular arrhythmias. A genetic mutation is found in up to 50-60% of probands, mostly affecting desmosomal genes. Diagnosis of AC is made by a combination of data from different modalities including imaging, electrocardiogram, Holter monitoring, family history, genetic testing, and tissue properties. Being a progressive cardiomyopathy, repeated cardiac imaging is needed in AC patients. Repeated imaging is important also for risk assessment of ventricular arrhythmias. This expert consensus document gives clinical recommendations for how to use multi-modality imaging in the different aspects of AC disease, including diagnosis, family screening, follow-up, risk assessment, and differential diagnosis.
Disciplines :
Cardiovascular & respiratory systems
Author, co-author :
Haugaa, KH; Oslo University Hospital > Cardiology
Basso, C; University of Padua Medical School > Cardiac, Thoracic and Vascular Sciences
Badano, LP; University of Padua Medical School > Cardiac, Thoracic and Vascular Sciences
Bucciarelli-Ducci, C; University Hospitals Bristol NHS Trust > Cardiology
Cardim, Nuno; Hospital da Luz > Cardiology
Gaemperli, O; University Heart Center Zurich > Interventional Cardiology and Cardiac Imaging
Galderisi, Maurizio; Federico II University Hospital > Advanced Biomedical Sciences
Habib, G; La Timone Hospital > Cardiology
Knuuti, J; Turku University Hospital > PET Centre
Lancellotti, Patrizio ; Université de Liège > Département des sciences cliniques > Imagerie cardiaque fonctionnelle par échographie
McKenna, W; Heart Hospital
Neglia, D; CNR Institute of Clinical Physiology and Scuola Superiore San'Anna > Cardiovascular
Popescu, Bogdan Alexandru; University of Medicine and Pharmacy "Carol Davila"
Edvardsen, Thor; Oslo University Hospital > Cardiology
Comprehensive multi-modality imaging approach in arrhythmogenic cardiomyoapthy : an expert consensus document of the European Association of Cardiovascular Imaging
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