Une présentation rare de craniosténose associée à un crâne lacunaire

[fr] Résumé : Le crâne lacunaire correspond à une description radiologique caractérisée par la présence de lacunes dans la voûte crânienne. Sa physiopathologie est, jusqu’à présent, mal comprise; il est le plus souvent accompagné par des anomalies du tube neural. L’association d’un crâne lacunaire avec une craniosténose est peu décrite dans la littérature. Nous rapportons le cas d’un patient âgé de neuf mois présentant une craniosténose multisuturaire compliquée d’un crâne lacunaire. Le traitement chirurgical a permis de remodeler le crâne et d’espérer une régression spontanée des lacunes.
[en] A rare case of lacunar skull deformity associated with craniosynostosis Summary : The lacunar skull is a radiologic description characterised by the presence of lacunae in the cranial vault. Its physiopathology remains up to now poorly understood; it is mostly associated with neural tube defects. The association of a lacunar skull with a craniosynostosis has rarely been described in the literature. The case of a 9-month-old patient presenting a multisutural craniosynostosis with a lacunar skull is reported in this article. The surgical treatment allowed to remodel the skull and to hope for a spontaneous regression of the lacunae.

Disciplines :

Pediatrics
Neurology

Author, co-author :

VAESEN, François ; Centre Hospitalier Universitaire de Liège - CHU > Département de chirurgie > Service d'urologie

Thimmesch, Mathieu; Université de Liège - ULiège > Pedaitrie > Service universitaire de Pédiatrie

BORN, Jacques; Centre Hospitalier Régionale de la Citadelle (Liège) - CHR CITADELLE > neurochirurgie

MISSON, Jean-Paul ; Centre Hospitalier Universitaire de Liège - CHU > Service de pédiatrie (CHR)

Language :

French

Title :

Une présentation rare de craniosténose associée à un crâne lacunaire

Alternative titles :

[en] A rare case of lacunar skull deformity associated with craniosynostosis

Publication date :

2016

Journal title :

Revue Médicale de Liège

ISSN :

0370-629X

eISSN :

2566-1566

Publisher :

Université de Liège. Revue Médicale de Liège, Liège, Belgium

Volume :

Issue :

Pages :

120-123

Peer reviewed :

Peer reviewed

Available on ORBi :

since 01 April 2016

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Bibliography

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