The abstract was presented by Dr. JF Kaux at the Annual Congress of the Royal Belgian Society of Physical and Rehabilitation Medicine (RBSPRM), in Brussels, Belgium, 2nd December 2005.
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[en] Introduction: In Joint Hypermobility Syndromes, chronic pain is the most disabling symptom. Its origin can be multiple (i.e. subluxations, sprains, pathologies of tendons, ligaments, peripheral nerves, multiple operations). The goal of this article was intended to discuss appropriate physiotherapy in hyperlax patients.
Patients and Method: The recovery process was analyzed in three cases (Marfan Syndrome, Ehlers-Danlos Syndrome and Osteogenesis Imperfecta). Hypermobility was assessed using the Brighton scale, pain using the Visual Analogue Scale and quality of life using the Medical Outcome Study Short Form-36. Bone density was evaluated by QDR X-ray absorptiometry. We emphasized that it was important to avoid stretching and to train the patient within a controlled range of motion. Submaximal eccentric exercises within a safe range of motion were incorporated to increase the active control of the joint positioning. Thus, in one patient, isokinetic rehabilitation was successfully undertaken. Each treatment had to be adapted to the individual patient and had to include specific home exercises.
Conclusion: In each case, physiotherapy gave good results in relation to pain, quality of life and stability of rehabilitated joints. Safety must be assured and specific evaluations such osteodensitometry, cardiac explorations and interventions of bracing, proprioceptive and functional strengthening can be very helpful.
Disciplines :
Rheumatology Human health sciences: Multidisciplinary, general & others Pediatrics Orthopedics, rehabilitation & sports medicine
Author, co-author :
Kaux, Jean-François ; Université de Liège - ULiège > Département des sciences de la motricité > Médecine physique et réadaptation fonctionnelle
Foidart-Dessalle, Marguerite ; Université de Liège - ULiège > Département des sciences de la motricité > Biomécanique
Croisier, Jean-Louis ; Université de Liège - ULiège > Médecine de l'appareil locomoteur
Toussaint, Geoffrey ; Université de Liège - ULiège > Médecine de l'appareil locomoteur
Forthomme, Bénédicte ; Université de Liège - ULiège > Département des sciences de la motricité > Rééducation du membre supérieur
Crielaard, Jean-Michel ; Université de Liège - ULiège > Département des sciences de la motricité > Evaluation et entraînement des aptitudes physiques - Médecine physique et réadaptation fonctionnelle
Language :
English
Title :
Physiotherapy Intervention for Joint Hypermobility in Three Cases with Heritable Connective Tissue Disorders
Publication date :
October 2010
Journal title :
Journal of Musculoskeletal Pain
ISSN :
1058-2452
eISSN :
1540-7012
Publisher :
Haworth Press, Binghamton, United States - New York
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