Abnormalities, Multiple/pathology; Autopsy; Brain/abnormalities; Cerebral Arteries/abnormalities; Circle of Willis/abnormalities; Female; Frontal Lobe/abnormalities; Humans; Infant, Newborn
Abstract :
[en] An infant with multiple congenital anomalies was found at autopsy to have a porencencephalic defect on the ventral surface of the left frontal lobe. The intracranial defect was seen in association with an anomalous configuration of the circle of Willis. The zone of tissue destruction corresponded to the vascular territory of the anterior choroidal and lenticulo-striate branches of the proximal middle cerebral arteries, which were absent on the left. The developmental anomaly of the circle of Willis may have predisposed to tissue destruction by compromising cerebral perfusion at midgestation, a stage of rapid brain growth.
Disciplines :
Neurosciences & behavior Neurology
Author, co-author :
Stewart, R. M.
Williams, R. S.
Lukl, P.
Schoenen, Jean ; Université de Liège - ULiège > Département des sciences biomédicales et précliniques > Neuro-anatomie
Language :
English
Title :
Ventral porencephaly: a cerebral defect associated with multiple congenital anomalies.
Publication date :
1978
Journal title :
Acta Neuropathologica
ISSN :
0001-6322
eISSN :
1432-0533
Publisher :
Springer Verlag, New York, United States - New York
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